Is Myopericytoma benign?
A rare, slow-growing soft tissue tumor that begins in cells that wrap around blood vessels. Most myopericytomas are benign (not cancer). They can occur anywhere in the body, but usually occur in the legs, trunk (chest and abdomen), or head and neck.
What is a Myofibroma?
Myofibroma is a solitary nodular tumor of the soft tissue, bone, or internal organs that affects all ages. The tumor may present as single or multiple nodules.
What is Glomangiopericytoma?
Glomangiopericytoma (GPC) is a rare vascular neoplasm of the nasal cavity and paranasal sinuses characterized by a pattern of prominent perivascular growth . GPC comprises less than 0.5% of all sinonasal neoplasia .
What is glomus Tumour?
Glomus tumors, or paragangliomas, are slow-growing, usually benign tumors in the carotid arteries (major blood vessels in your neck), the middle ear or the area below the middle ear (jugular bulb). Glomus tumors are most often benign; however, they can cause significant damage to surrounding tissues as they grow.
Can Myofibroma be cancerous?
IM tumors are benign, which means they are not cancer and do not spread to other parts of the body. But these tumors may grow large and damage nearby organs.
What causes a Myofibroma?
Most cases of infantile myofibromatosis occur randomly, for no apparent reason. Rare familial cases (in which more than one family member is affected) have been identified and genetic changes (mutations) in two different genes (PDGFRB and NOTCH3) have been found to cause the condition in most of these cases.
Is Glomangiopericytoma malignant?
This tumor differs from conventional soft tissue hemangiopericytoma in location, biologic behaviour and histologic features. Glomangiopericytoma is a borderline low malignancy tumor with a good prognosis after complete surgical resection.
How do you know if you have a glomus tumor?
Imaging studies — Glomus tumors of the head and neck are diagnosed primarily through MRI and CT scans. The specific locations of these tumors are usually sufficient for a diagnosis. Angiograms — Because of their vascular nature, your doctor may also order an angiogram to confirm the diagnosis of glomus tumors.
How common is a glomus tumor?
A glomus tumor (also known as a “solitary glomus tumor,” “solid glomus tumor,”) is a rare neoplasm arising from the glomus body and mainly found under the nail, on the fingertip or in the foot. They account for less than 2% of all soft tissue tumors.
How common is Myofibroma?
How common is infantile myofibromatosis? IM is found at birth in about 1 out of 150,000 babies. Some cases of IM may not be diagnosed or correctly diagnosed.
What is myofibroblastic tumor?
An inflammatory myofibroblastic tumor (IMT) is an uncommon, usually benign (non-cancerous) tumor made up of cells called myofibroblastic spindle cells. It usually develops in children or young adults, but can affect people of any age.
What’s the difference between myofibroma and myopericytoma?
Myopericytoma is a unifying term for a group of histologically overlapping lesions, which span a spectrum from infantile HPC (most likely representing the cellular phase of myofibroma in young children), to adult myofibroma and infantile myofibromatosis, to somewhat more glomoid-appearing lesions, termed myopericytoma and glomangiopericytoma.
Are there any intraosseous myofibromas in adults?
Intraosseous myofibromas are very rare and are typically destructive lesions that predominantly affect craniofacial bones in the setting of myofibromatosis. Solitary, intraosseous myofibromas in adults are exceedingly rare.
What kind of surgery is needed for myopericytoma?
Myopericytoma is a benign tumor that rarely recurs following marginal or even intralesional excision. Simple surgical excision is adequate treatment. Which of the following is true about myofibroma / myofibromatosis? A 38 year old man presented with a left thigh mass.
What are the atypical features of myopericytomas?
Small subset of myofibromas / myopericytomas shows atypical features (diffuse hypercellularity, infiltrative growth pattern and increased mitotic figures) that do not adversely affect outcome ( Am J Surg Pathol 2014;38:1649 ) 64 year old woman with a mass at the craniocervical junction ( Neurosurgery 2019;85:E360 )